Ollier's
disease
Clinical
Findings
-
Usually appears in the first decade of life
- Palpable bony mass
- Asymmetric shortening of the extremities
-
Osseous deformity related to fracture
Clinical Course
of Enchondroma
- Disappear during growth and displaced by normal bone
- Do not increase unless malignant transformation,
after
cessation of growth
Involving sites
- Most frequently, long tubular bone (tibia, femur, fibula)
- Less frequently, metacarpal,metatarsal bone
- Flat bone : pelvis, rib
Complications
- In childhood : pathologic fracture
- In adult : malignant transformation
- Most frequently in femur
Imaging
Findings
-
Plain : multiple, well-defined, lobulated, medullary osteolytic tumor
with/without calcification in cartilaginous matrix
-
MR : low SI on T1WI, high SI on T2WI

Malignant
Transformation (5 to 30%)
- Most frequently, chondrosarcoma
- Less frequently, dedifferentiated chondrosarcoma,
osteosarcoma or chondroid chordoma
- Imaging Findings
1. More than 8 cm
2. Pain, soft tissue mass
3. Disappearance of pre-existing calcification
4. Radiolucent area
5. Pathologic fracture