Ollier's disease


Clinical Findings
        - Usually appears in the first decade of life

        - Palpable bony mass

        - Asymmetric shortening of the extremities

        - Osseous deformity related to fracture

  Clinical Course of Enchondroma

        - Disappear during growth and displaced by normal bone

        - Do not increase unless malignant transformation,

      after cessation of growth
 

  Involving sites

        - Most frequently, long tubular bone (tibia, femur, fibula)

        - Less frequently, metacarpal,metatarsal bone

        - Flat bone : pelvis, rib

 

  Complications

        - In childhood : pathologic fracture

        - In adult : malignant transformation

        - Most frequently in femur


Imaging Findings

        - Plain : multiple,  well-defined, lobulated, medullary osteolytic tumor with/without calcification in  cartilaginous matrix

        - MR : low SI on T1WI, high SI on T2WI  


case1h.jpg case1i.jpg case1k.jpg


Malignant Transformation (5 to 30%)

        - Most frequently, chondrosarcoma

        - Less frequently, dedifferentiated chondrosarcoma,

                     osteosarcoma or chondroid chordoma

 

        - Imaging Findings

                1. More than 8 cm

                2. Pain, soft tissue mass

                3. Disappearance of pre-existing calcification

                4.  Radiolucent area

                5. Pathologic fracture


Return to Images