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대한흉부영상의학회 Weekly Case 검색
대한흉부영상의학회 Weekly Case 검색
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Weekly Chest CasesImaging Conference Cases

Case No : 9

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  • Age/Sex 24 / F
  • Case Title 24-year-old woman with skin lesion and seizure
  • Figure 1
  • Figure 2
  • Figure 3

Diagnosis With Brief Discussion

Courtesy
Asan Medical Center
Discussion
Tuberous Sclerosis
- AD disorder of mesodermal development (Chr 9)
- Classical triad
- Epilepsy, mental retardation, adenoma sebaseum

Lung involvement
- Uncommon (1- 2.5%)
- Female predominent
- Similar to LAM
- Chest radiograph: Diffuse reticular pattern c/s cystic or bullous changes
- HRCT: Thin-walled cysts of various size through both lungs
- Pneumothorax is common (50%)
- Chylous pleural effusion
- pneumodediastinum

Micronodular pneumocyte hyperplasia
- Widespread, evenly distributed nodules
- 1-3 mm (up to 8 mm) on HRCT
- Represent hamartomatous proliferation of type 2 pneumocytes
- May affect male TS patients (unlike LAM)
(Br J Radiol. 2000 ;73 :91-8)
Keywords
Lung, Interstitial lung disease, Tuberous sclerosis,
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Current Editor : Sung Shine Shim, MD, PhD. Email : sinisim@ewha.ac.kr

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