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대한흉부영상의학회 Weekly Case 검색
대한흉부영상의학회 Weekly Case 검색
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Weekly Chest CasesImaging Conference Cases

Case No : 5

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  • Age/Sex 44 / M
  • Case Title 44-year-old man with dyspnea for 3 months, Recurrent left pneumothorax
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Diagnosis With Brief Discussion

Courtesy
Ewha Womans University Mokdong Hospital
Discussion
Langerhans cell histiocytosis (histiocytosis X, eosinophilic granuloma)
- Early stage : nodular collections of Langerhans histiocytes and eosinophils (juxtabronchiolar )
- Late stage : fibrosis, honeycombing

- young or middle-aged adults, male predominance, ciagrette smoking history (> 90%), pneumothorax (14%)
- variable PFT pattern/ decreased diffusing capacity
- 60% (lung), 40% (lung + bone, other organ)
- Px : 1/2 favorable, 1/3 stable, 20% progress ( respiratory failure, pulmonary a. HT)

CXR
- nodular, reticulonodular, and cystic abnormalities (upper lung >>)

Evolution on CT
Nodule (1-5mm, centrilobular and peribronchiolar) -> cavitary nodule & thick-walled cyst -> cyst (large confluent, bizarre) -> GGA, irregular lines & honeycombing

End-stage lung disease
- UIP (43%), sarcoidosis (15%), HX (13%), asbestosis, EAA, silicosis, LAM
Keywords
Lung, Interstitial lung disease, LCH,
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Each Case of This Site Supplied by the Members of KSTR.
Copyright of the Images is in the KSTR and Original Supplier.
Current Editor : Sung Shine Shim, MD, PhD. Email : sinisim@ewha.ac.kr

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