Discussion
Diagnosis With Brief Discussion
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- Differential Diagnosis
- Lymphocytic interstitial pneumonia
Lymphangioleiomyomatosis
Langerhans cell histiocytosis
Pulmonary cystic metastasis
Bronchioloalveolar carcinoma
Sarcoidosis
- Discussion
- Clinical Laboratory findings
- Dry eyes & Dry mouth
- Anti-SSa / Anti-SSb(+/+)
Chest radiograph
- multuiple pulmonary cysts of variable size
- Basilar predominance
- Prominent peribronchovascular marking
- Ill-defined nodular opacities
Chest CT
- Multiple thin-walled lung cysts of various sizes
- Random distribution, basilar predominance
- Nodular opacities, some of them having CT halo sign
- No thickening of BVB or interlobular septa
- Small mediastinal lymph nodes
- No pleural effusion
- Keywords
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Lung, Airway, Interstitial lung disease, Metabolic and storage lung disesae,