Weekly Chest CasesImaging Conference Cases

Case No : 7

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  • Age/Sex 53 / M
  • Case Title Dyspnea
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Diagnosis With Brief Discussion

Courtesy
S
Definitive Diagnosis
Mediastinoscopic biopsy
Imaging Findings

????????????Diffuse infiltrating soft tissue lesion

      • All compartment of the mediastinum
      • Obliterates normal mediastinal fat planes
      • Encases or encoarch adjacent structure
Reviewy

????????????????????Etiology:

        • Idiopathic
        • Granulomatous infection: Histoplasma capsulatum

        ?

        ????????????Affected patients: typically young

        ?

        ????????????Two types

        ????????????????Focal type(82%):

            • Localized, calcified mass in the paratracheal or subcarinal regions of the mediastinum or pulmonary hila

        ?

        ????????????????Diffuse type(18%):

            • Diffuse infiltrating, non-calcified mass
            • Affects multiple mediastinal compartments

        ?

        ????????????Fibrosing mediastinitis is the most likely diagnosis

            • Extensive calcified, infiltrative mediastinal mass
            • Young patients, Endemic area for histoplasmosis

?

    ????????????Differential diagnosis

        • DDx: Lung cancer, Metastatic carcinoma, Lymphoma, Mediastinal sarcoma, Mediastinal desmoid tumor

    ?

    ????????????Treatment and prognosis: unpredictable course

        • Spontaneous remission or Exacerbation
        • Mortality rate: 30%
        • Subcarinal or bilateral mediastinal involvement : much higher motality

    ????????????????????????????????????????????????????????????????????????????????????(RadioGraphics 2001; 21:737-757)

    Keywords
    Mediastinum, Non-infectious inflammation, Fibrosing Mediastinitis, Diffuse Type
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