Discussion
Diagnosis With Brief Discussion
- Diagnosis
- Partial Anomalous Pulmonary Venous Return
- Radiologic Findings
- Contrast enhanced CT scans and volume rendering 3D image show left superior pulmonary vein enters left brachiocephalic vein along the lateral aspect of the aortic arch. Left inferior pulmonary vein is normally drained into left atrium.
- Brief Review
- Anomalous pulmonary vein drainage involves drainage of a pulmonary vein branch into the right atrium, coronary sinus, or systemic vein, producing a left-to-right shunt.
Patients are most frequently asymptomatic. The extent of symptoms and physiologic disturbances are dependent on the degree of shunting, the number of anomalous veins, any associated valvular abnormalities, and the presence of any concomitant cardiac or pulmonary disease. Surgical correction is recommended for symptomatic patients or asymptomatic patients with a pulmonary-to-systemic blood flow ratio exceeding 1.5 because of their higher likelihood of progression to pulmonary hypertension and right ventricular failure.
Partial Anamalous pulmonary vein drainage is present in about 0.5% of the population. The anomalous vein may drain into various vascular structures. On the right, the most common are the superior vena cava, azygos vein, inferior vena cava, and right atrium. On the left, drainage may be through the left brachiocephalic vein, persistant left superior vena cava, or coronary sinus. Drainage may be also below the diaphragm. In the scimitar syndrome, the aberrant drainage of the right pulmonary vein occurs the below the diaphragm, often into the inferior vena cava.
Total anomalous pulmonary venous drainage must be associated with a septal defect and is best considered to be a type of congenital heart disease.
- References
- 1. Webb WR. Congenital bronchopulmonary lesions In. Webb WR, Higgins CB. Thoracic imaging, Philadelphia: LWW, 2005 1-29
2. Naidich DP, M?ler NL, et al. Pulmonary arteries and hilar In. Computed tomography and magnetic resonance of the thorax. 1999 603-656
3. AboulHosn JA, Crilev JM, Stringer WW. Partial anomalous pulmonary venous return: case report and review of the literature.
Catheter Cardiovasc Interv. 2003 Apr;58(4):548-52.
- Keywords
- Vascular, Vascular,