Discussion
Diagnosis With Brief Discussion
- Diagnosis
- Achalasia
- Radiologic Findings
- Posteroanterior chest radiograph shows a huge mass-like opacity with air-fluid level in right paratracheal and paravertebral area. The right heart silhouette is intact.
Axial images of contrast-enhanced chest CT also show diffuse, extensive dilatation of esophagus with food stagnation
- Brief Review
- Achalasia is a well-recognized esophageal motility disorder characterized by a combination of absent peristalsis in the thoracic esophagus and impaired opening of the lower esophageal sphincter (LES) in response to deglutition. Two major forms of achalasia have been described: primary and secondary. The primary or idiopathic form is caused by degeneration of myenteric plexi in the wall of the esophagus. The etiology of this neural degeneration remains unknown but is postulated to be secondary to viral or autoimmune disease. In contrast, secondary achalasia (also known as pseudo-achalasia) is a less common form caused by extra-esophageal conditions (especially malignant tumors) that induce an achalasia-like motility disorder by a variety of proposed mechanisms.
Characteristic imaging findings are as follows; 1) huge mass shadow in right paracardiac area with intact right heart silhouette on chest radiograph, 2) Markedly dilated esophagus with mild diffuse wall thickening on CT and 3) markedly distended esophageal lumen with abrupt but smooth tapering at GE junction level (terminal beak sign) on esophagography.
- References
- 1. Diseases of the Esophagus: Diagnosis with Esophagography Radiology 2005; 237:414–427
2. Achalasia: new perspectives on an old disease Neurogastroenterol Motil 2016; 28, 4–11
- Please refer to
- Case 112 Case 961
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- Keywords
- Esophagus, Others,