Discussion
Diagnosis With Brief Discussion
- Diagnosis
- Poland syndrome
- Radiologic Findings
- Chest radiograph shows slightly hyperlucent left lung (Fig. 1). CT scan demonstrates absence of the left pectoralis major and minor muscles (Fig. 2,3).
- Brief Review
- Poland syndrome is a rare congenital anomaly characterized by hypoplasia of the breast and nipple, scarcity of subcutaneous tissue, absence of the costosternal portion of the pectoralis major muscle, lack of the pectoralis minor muscle, aplasia or deformity of the costal cartilages or ribs II to IV or III to V, alopecia of the axillary and mammary region, and unilateral brachysyndactyly. The condition is more frequent among males, and usually occurs on the right hemithorax in the unilateral form.
. Chest radiography reveals an area of hyperlucency on the affected side that mimics a radical mastectomy or Swyer-James syndrome. CT more clearly depicts the absence of pectoralis major muscle and allows better appreciation of other associated musculoskeletal anomalies.
- Please refer to
Case 490, -
- References
- 1. Fokin, Alexander A., and Francis Robicsek. Poland syndrome revisited. The Annals of thoracic surgery 74.6 (2002): 2218-2225.
2. Jeung, Mi-Young, et al. "Imaging of chest wall disorders." Radiographics 19.3 (1999): 617-637.
- Keywords
- Poland syndrome , Chest wall, Pectoralis muscle,