대한흉부영상의학회 Weekly Chest Cases

Diagnosis: IgG4-related lung disease
Radiologic Findings: Fig 1. Chest PA shows diffuse mass-like consolidations in RULZ, RLLZ and LLLZ
Fig 2-4. CT scans reveal multifocal nodular consolidations in subpleural and peribronchial area with CT angiogram sign, and enlarged LNs in subcarinal, paratracheal areas
Fig 5. Strong FDG uptake (SUVmax: 14) in the lung lesions and enlarged LNs
Brief Review: IgG4-related lung disease
:Fibro-inflammatory condition that can affect multi-organs

Pathology : Diffuse lymphoplasmacytic infiltration with fibrosis
No necrosis or granulomatous inflammation
Serum IgG4 level is correlated with disease activity

Parenchymal : nodule/masses, interstitial lung disease
Airways : tracheobronchial stenosis
Pleural : nodules/effusion
Mediastinal :lymphadenopathy, fibrosing mediastinitis

Image findings: parenchymal types
Solid nodular type
Round GGO type
Alveolar interstitial type
Bronchovascular type
References: Respirology, Volume18, Issue3 April 2013 Pages 480-487
BMC Pulmonary Medicine volume 16, Article number: 20 (2016)
La radiologia medica volume 124, pages 1262–1269 (2019)
Semin Respir Crit Care Med 2020;41:202–213.
Radiographics : a review publication of the Radiological Society of North America, Inc. 32 (1): 51-69.
Keywords

대한흉부영상의학회 Korean Society of Thoracic Radiology