Discussion
Diagnosis With Brief Discussion
- Diagnosis
- Mediastinal plexiform neurofibromatosis
- Radiologic Findings
- Brief Review
- Chest radiograph shows mediastinal widening and notching of left 3rd rib. Rib notching in this clinical situation is highly suggestive of mass arising from intercostal nerve although infracostal mass is not definitely seen in this case.
CT reveals multicompartmental mediastinal lesions of low attenuation (less than muscle) and bilateral nipple-like protrusion abutting the heart, which correspond to the course of the phrenic nerves. In the appropriate clinical setting, CT detection of lesions in the distribution of the mediastinal nerves strongly favors the diagnosis of plexiform neurofibromatosis.
- References
- Bourgouin PM, Shepard JO, Moore EH, McLoud TC. Plexiform neurofibromatosis of the mediastinum: CT appearance. AJR 1988;151:461-463
- Keywords
- Mediastinum, Chest wall, Benign tumor, Mediastinal plexiform neurofibromatosis