Discussion
Diagnosis With Brief Discussion
- Diagnosis
- Poland syndrome
- Radiologic Findings
- Chest radiograph shows slightly hyperlucent right lung (Fig. 1). CT scan demonstrates absence of the right pectoralis major and minor muscles, and small right breast (Fig. 2,3).
- Brief Review
- Poland syndrome is a congenital anomaly consisting of aplasia or hypoplasia of pectoralis major muscle with ipsilateral syndactyly. Occasionally other malformations of the anterior chest wall and breast including absence or atrophy of the ipsilateral second to fifth ribs, absence of pectoralis minor muscle, aplasia of the ipsilateral breast or nipple, and simian crease of the affected extremity may be associated. The condition is more frequent among males, and usually occurs on the right hemithorax in the unilateral form.
Chest radiography reveals an area of hyperlucency on the affected side that mimics a radical mastectomy or Swyer-James syndrome. CT more clearly depicts the absence of pectoralis major muscle and allows better appreciation of other associated musculoskeletal anomalies.
- References
- 1. Jeung MY, Gangi G, Gasser B, et al. Imaging of Chest Wall Disorders. Radiographics.1999;19:617-637
2. Ferraro GA, Perrotta A, Rossano F, DAndrea F. Poland syndrome: description of an atypical variant. Aesthetic Plast Surg. 2005;29:32-33. Epub 2005 Mar 10.
- Keywords
- Chest wall, Congenital,